Document Type : Case Report(s)

Authors

• Sanjay Yadav ¹
• Chandan Kumar Jha ²
• Saroj Kanta Mishra ¹
• Ritu Verma ³
• Abhishek Krishna ¹

¹ Department of Endocrine Surgery, Sanjay Gandhi PG Inst. of Medical Sciences, Lucknow, India

² Department of General Surgery, All India Institute of Medical Sciences, Patna, India

³ Department of Pathology, Sanjay Gandhi PG Inst. of Medical Sciences, Lucknow, India

Abstract

Adrenocortical carcinoma (ACC) is a very rare disease in the pediatric age group. The clinic-biological profile, histopathological criteria of diagnosis, and staging of this disease in this age group are different from those of adult ACC. In this paper, we report a case of pediatric ACC presenting as Cushing syndrome that was managed with complete surgical excision. Through this case presentation, we highlight the sequential protocol of investigations and management in a child suspected of having ACC.

Keywords

• Pediatric ACC
• Cushing’s syndrome