Pediatric Mixed Functioning Adrenocortical Carcinoma: A Case Report and Review of Literature

Yadav, Sanjay; Jha, Chandan Kumar; Mishra, Saroj Kanta; Verma, Ritu; Krishna, Abhishek

doi:10.30476/mejc.2019.78633.

Pediatric Mixed Functioning Adrenocortical Carcinoma: A Case Report and Review of Literature

Document Type : Case Report(s)

Authors

Sanjay Yadav ¹

Chandan Kumar Jha ²

Saroj Kanta Mishra ¹

Ritu Verma ³

Abhishek Krishna ¹

¹ Department of Endocrine Surgery, Sanjay Gandhi PG Inst. of Medical Sciences, Lucknow, India

² Department of General Surgery, All India Institute of Medical Sciences, Patna, India

³ Department of Pathology, Sanjay Gandhi PG Inst. of Medical Sciences, Lucknow, India

https://doi.org/10.30476/mejc.2019.78633.

Abstract

Adrenocortical carcinoma (ACC) is a very rare disease in the pediatric age group. The clinic-biological profile, histopathological criteria of diagnosis, and staging of this disease in this age group are different from those of adult ACC. In this paper, we report a case of pediatric ACC presenting as Cushing syndrome that was managed with complete surgical excision. Through this case presentation, we highlight the sequential protocol of investigations and management in a child suspected of having ACC.

Keywords

Pediatric ACC

Cushing’s syndrome