%0 Journal Article %T Primitive Neuroectodermal Tumor of the Kidney in a 22-Year-Old Male: A Rare Entity %J Middle East Journal of Cancer %I Shiraz University of Medical Sciences %Z 2008-6709 %A Gupta, Veena %A Sen, Rajeev %A Batra, Ashima %A Jain, Promil %D 2014 %\ 10/01/2014 %V 5 %N 4 %P 233-236 %! Primitive Neuroectodermal Tumor of the Kidney in a 22-Year-Old Male: A Rare Entity %R %X Primitive neuroectodermal tumors of the kidney are rare tumors representing about 1% of all sarcomas. Extraskeletal primitive neuroectodermal tumors may be found in the genitourinary tract, the testes, ovaries, uterus, or pancreas. Renal primitive neuroec- todermal tumors are frequently aggressive and almost 30% of all newly diagnosed cases present with distant metastases. Surgical intervention, intensive chemotherapeutic drugs and radiation therapy are the best choices for management. We discuss the case of a 22-year-old male who presented with a left renal mass. He underwent nephrectomy followed by histopathological examination. Microscopic and immunohistochemical examination revealed a primitive neuroectodermal tumor. %U https://mejc.sums.ac.ir/article_41974_0183ef035bb98ccd9718e757be6c068a.pdf