Document Type: Case Report

Authors

1 Department of Endocrine Surgery, Sanjay Gandhi PG Inst. of Medical Sciences, Lucknow, India

2 Department of General Surgery, All India Institute of Medical Sciences, Patna, India

3 Department of Pathology, Sanjay Gandhi PG Inst. of Medical Sciences, Lucknow, India

Abstract

Adrenocortical carcinoma (ACC) is a very rare disease in the pediatric age group. The clinic-biological profile, histopathological criteria of diagnosis, and staging of this disease in this age group are different from those of adult ACC. In this paper, we report a case of pediatric ACC presenting as Cushing syndrome that was managed with complete surgical excision. Through this case presentation, we highlight the sequential protocol of investigations and management in a child suspected of having ACC.

Keywords